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Vol. 68. Issue 2.
Pages 170-171 (February 2015)
DOI: 10.1016/j.rec.2014.10.007
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Correction in article “Familial Left Ventricular Noncompaction Associated With a Novel Mutation in the Alphacardiac Actin Gene”, Rev Esp Cardiol. 2014;67:857-9
Correcci??n en el art??culo ??Miocardiopat??a no compactada familiar asociada con una mutaci??n nueva en el gen de la alfa actina cardiaca??, Rev Esp Cardiol. 2014;67:857-9
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Table. Results From the Clinical Family Evaluation
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In the article by Rodríguez-Serrano et al., “Familial Left Ventricular Noncompaction Associated With a Novel Mutation in the Alphacardiac Actin Gene”, published in Rev Esp Cardiol. 2014;67:857-9, the following errors were found:

Figure. In the last line of the family pedigree, where it says: “V: 1”, it should say: “IV:1”. The correct figure is:

Table. Row 7 has been duplicated by mistake. The characteristics of rows 4 and 6 (pedigree positions III:4 and III:6) have been switched. The correct table is:


Results From the Clinical Family Evaluation

Pedigree position  Sex/Age, y  Clinical history  ECG  Echocardiography  CMRI  Holter  Exercise testing  Genetics: heterozygous ACTC1I289T mutation 
II:3  F/59  Asymptomatic  Normal  Normal  —  —  —  Non carrier 
II:4  M/66  Dyspnea, NYHAclass I-II/IV  SR, first degree AV block, QS in the inferior leads  One year before this study, in another center: echocardiography within normal limitsAt the beginning of this study: LVNC, normal LV size; LVEF, 36%; moderately impaired RVEFAt follow-up: upper limit LV diameters with hypertrabeculation; LVEF, 25%; normal RVEF  LVNC; LVEF, 48%; intramyocardial LGE at the inferior wall and posterior septum  SR, unremarkable isolated ventricular ectopies, unremarkable atrial ectopies in isolation, couplets and salvoes  Normal  Carrier 
III:2  F/33  Asymptomatic  Normal  Normal  —  —  —  Non carrier 
III:4  M/31  Dysnea, NYHA class II/IV  SR, nonspecific ventricular activation delay  LVNC; spheric-shaped dilated LV (65/52 mm); LVEF, 25%; restrictive filling pattern; severe mitral regurgitation; normal-sized RV with preserved RVEF  LVNC; dilated LV; LVEF, 27%; prolapse of posterior mitral left with severe mitral regurgitation.  SR; scarce atrial ectopies in couplets and salvoes; ventricular ectopies in isolation (1908); couplets (43), and one salvoe (5 beats)  Ventricular ectopies and 1 nonsustained ventricular tachycardia (3 beats) at peak exercise  Carrier 
III:5  M/37  Asymptomatic  Normal  Normal  —  —  —  Non carrier 
III:6  F/32  Previous clinical history: OS-ASD repaired at 10 years of age; one miscarriage (hydrops)At follow-up: Dyspnea class I-II/IV NYHA  Normal  Three years before this study, in another center: echocardiography within normal limitsAt the beginning of this study: normal LV size; LVEF, 53%; apical and septal hypertrabeculation, restrictive filling pattern normal sized RV with mildly impaired RVEFAt 1-year follow-up: upper limit LV diameters (51/43 mm); LVEF, 36%; restrictive filling pattern; apical hypertrabeculation not fullfilling criteria for LVNC; moderate tricuspid regurgitation without pulmonary hypertension. upper limit RV diameters with mildly impaired RVEFAt 2-year follow-up: improvement of LVEF and RVEF  Three years before this study, in another center: hypertrabeculation in lateral and inferolateral regions; normal sized LV; LVEF, 51%At the beginning of this study: LVNC more prominent at the anterolateral and inferolateral wall; dilated LV; LVEF, 55%; RVEF, 46%; subepicardial LGE at the inferior and lateral walls; akinetic biventricular apical segments  SR, isolated rare atrial and ventricular ectopies  Normal  Carrier 
IV:1  F/3  Heart transplantation at 9 months of age because of refractory heart failure; no further clinical events  SR at 150 bpm; left atrial and LV hypertrophy and inespecific alteration in the ventricular repolarization  Before heart transplantation:dilated LV (36/27 mm) and LVEF, 46%; restrictive filling pattern; severe-moderate mitral and tricuspid regurgitation; moderate pulmonary hypertension; OS-ASD, 5 mmAt heart transplantation:LV hypertrabeculation  —  —  —  Carrier 

ACTC1, alpha-cardiac actin gene; AVB: atrioventricular block; CMRI, cardiac magnetic resonance imaging; ECG, electrocardiogram; F, female; LGE, late gadolinium enhancement; LV, left ventricle; LVEF, left ventricular ejection fraction; LVNC, left ventricular noncompaction; M, male; MI, myocardial infarction; NE, not evaluated; NYHA, New York Heart Association; OS-ASD, ostium secundum atrioseptal defect; RV, right ventricle; RVEF, right ventricular ejection fraction; SR: sinus rhythm.

These corrections were made in the electronic version of the article on 5 November 2014.

Copyright © 2014. Sociedad Española de Cardiología
Revista Española de Cardiología (English Edition)

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